DISEASE SCANNER

Global Incurable Diseases Tracker

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Cancer

Retinoblastoma

HIGH SEVERITY

The most common intraocular malignancy in children, caused by RB1 tumor suppressor gene mutations. Can be unilateral (usually non-hereditary) or bilateral (hereditary). Early detection critical for vision preservation and survival.

Global Affected

18.0K

Countries

15

Symptoms

Leukocoria (white pupillary reflex)
Strabismus
Eye redness
Poor vision
Eye pain (advanced)
Orbital mass (advanced)
Glaucoma (secondary)

Treatment Options

Surgery
Chemotherapy
Radiation therapy
Immunotherapy
Targeted therapy
Hormone therapy
Stem cell transplant
Palliative care

Risk Factors

1Age
2Family history
3Genetic mutations
4Smoking
5Alcohol consumption
6Obesity
7Physical inactivity
8Environmental exposures
9Infections (HPV, HBV, HCV, H. pylori)

Diagnostic Methods

  • 1Biopsy
  • 2Imaging (CT, MRI, PET)
  • 3Tumor markers
  • 4Genetic testing
  • 5Endoscopy
  • 6Blood tests
  • 7Screening programs

Prognosis

Intraocular disease has 95%+ cure rate with modern therapy (chemotherapy, focal therapy, enucleation). Group A-E classification guides treatment. Bilateral disease requires genetic testing; 90% have germline RB1 mutation with hereditary risk and increased lifetime second cancer risk. Metastatic disease has 50-60% survival with intensive chemotherapy. Long-term surveillance for second cancers (osteosarcoma, melanoma) in germline mutation carriers. Vision preservation possible in many unilateral and some bilateral cases.

Prevention

  • Smoking cessation
  • Sun protection
  • Healthy diet
  • Regular exercise
  • Vaccination (HPV, HBV)
  • Screening programs
  • Limit alcohol
  • Maintain healthy weight

Research Status

Focal laser, cryotherapy, and chemotherapy (systemic, intra-arterial, intravitreal). Eye salvage possible in 90%. Enucleation for advanced cases. Screening for hereditary form. 95% survival in developed countries.

Sources

  • https://www.cancer.gov
  • https://www.who.int/cancer
  • https://www.cancer.org

Medical Disclaimer

This information is for educational purposes only. Always consult healthcare professionals for medical advice, diagnosis, and treatment.