DISEASE SCANNER
Global Incurable Diseases Tracker
Idiopathic Pulmonary Fibrosis
A chronic, progressive, fibrosing interstitial pneumonia of unknown cause, occurring primarily in older adults. Characterized by progressive scarring of lung tissue. Median survival 3-5 years without treatment. Associated with telomerase gene mutations in some families.
3.0M
15
Symptoms
Treatment Options
Risk Factors
Diagnostic Methods
- 1Clinical evaluation
- 2Laboratory tests
- 3Imaging
- 4Functional assessments
- 5Patient-reported outcomes
- 6Screening questionnaires
Prognosis
Chronic conditions require ongoing management. With proper treatment and lifestyle modifications, most patients can maintain good quality of life.
Prevention
- Healthy lifestyle
- Regular exercise
- Balanced diet
- Stress management
- Avoidance of toxins
- Regular health screenings
Research Status
Antifibrotics nintedanib and pirfenidone slow decline in FVC. Lung transplant only definitive treatment. Triple therapy (prednisone/azathioprine/NAC) harmful. Anti-fibrotic combinations being studied.
Affected Countries
Sources
- https://www.who.int/chp
- https://www.cdc.gov/chronicdisease
- https://medlineplus.gov/chronicdiseases.html
Medical Disclaimer
This information is for educational purposes only. Always consult healthcare professionals for medical advice, diagnosis, and treatment.