DISEASE SCANNER

Global Incurable Diseases Tracker

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Cancer

Neuroblastoma

HIGH SEVERITY

The most common extracranial solid tumor in childhood, arising from neural crest cells of the adrenal medulla or sympathetic nervous system. Highly variable clinical behavior ranging from spontaneous regression to aggressive metastatic disease.

Global Affected

25.0K

Countries

15

Symptoms

Abdominal mass
Opsoclonus-myoclonus (paraneoplastic)
Periorbital ecchymosis
Horner syndrome
Bone pain
Weight loss
Hypertension
Diarrhea (VIP-secreting)

Treatment Options

Surgery
Chemotherapy
Radiation therapy
Immunotherapy
Targeted therapy
Hormone therapy
Stem cell transplant
Palliative care

Risk Factors

1Age
2Family history
3Genetic mutations
4Smoking
5Alcohol consumption
6Obesity
7Physical inactivity
8Environmental exposures
9Infections (HPV, HBV, HCV, H. pylori)

Diagnostic Methods

  • 1Biopsy
  • 2Imaging (CT, MRI, PET)
  • 3Tumor markers
  • 4Genetic testing
  • 5Endoscopy
  • 6Blood tests
  • 7Screening programs

Prognosis

Highly variable by risk stratification. Low-risk (infants with stage 4S, favorable biology): >95% survival with observation or minimal therapy. Intermediate-risk: 90-95% survival with moderate chemotherapy. High-risk (MYCN-amplified, age >18 months, metastatic): 40-50% survival despite intensive multimodal therapy. GD2 immunotherapy improves outcomes in high-risk disease. Late relapses occur; surveillance for 5+ years. Survivors face hearing loss, growth delay, and secondary malignancies.

Prevention

  • Smoking cessation
  • Sun protection
  • Healthy diet
  • Regular exercise
  • Vaccination (HPV, HBV)
  • Screening programs
  • Limit alcohol
  • Maintain healthy weight

Research Status

Surgery, chemotherapy, radiation, stem cell transplant. Immunotherapy (dinutuximab) and MIBG therapy. Observation alone for low-risk. Survival >95% for low-risk, 40-50% for high-risk. Genomic profiling guiding treatment.

Sources

  • https://www.cancer.gov
  • https://www.who.int/cancer
  • https://www.cancer.org

Medical Disclaimer

This information is for educational purposes only. Always consult healthcare professionals for medical advice, diagnosis, and treatment.