DISEASE SCANNER
Global Incurable Diseases Tracker
Nephrogenic Diabetes Insipidus
A kidney disorder where the kidneys cannot concentrate urine due to resistance to antidiuretic hormone (ADH/vasopressin). Causes excessive thirst and excretion of large amounts of dilute urine. Can be inherited (genetic) or acquired (lithium, other medications).
2.0M
89
Symptoms
Treatment Options
Risk Factors
Diagnostic Methods
- 1Water deprivation test
- 2Desmopressin challenge
- 3Serum/urine osmolality
- 4Genetic testing
- 5Renal ultrasound
- 6ADH level
Prognosis
Chronic condition requiring lifelong management. Acquired forms may improve if cause removed. Genetic forms permanent but manageable. Dehydration is main risk if not properly managed.
Prevention
- Avoid lithium if possible
- Regular monitoring on lithium
- Genetic counseling
- Early diagnosis
- Adequate hydration
- Avoid dehydration triggers
Research Status
Low-salt diet and thiazide diuretics paradoxically reduce urine output. NSAIDs (indomethacin) can help. Treat underlying cause if acquired. Adequate fluid intake essential. Genetic forms lifelong management.
Affected Countries
Sources
- https://www.niddk.nih.gov/health-information/kidney-disease/nephrogenic-diabetes-insipidus
- https://rarediseases.org/rare-diseases/nephrogenic-diabetes-insipidus
- https://www.kidney.org/atoz/content/diabetes-insipidus
Medical Disclaimer
This information is for educational purposes only. Always consult healthcare professionals for medical advice, diagnosis, and treatment.