DISEASE SCANNER
Global Incurable Diseases Tracker
Immune Thrombocytopenia (ITP)
An autoimmune disorder characterized by isolated low platelet count due to immune-mediated platelet destruction and impaired production. Formerly called idiopathic thrombocytopenic purpura. Acute form common in children, chronic in adults.
6.0M
19
Symptoms
Treatment Options
Risk Factors
Diagnostic Methods
- 1Complete blood count (isolated low platelets)
- 2Peripheral blood smear
- 3Bone marrow biopsy (if atypical)
- 4HIV, HCV testing
- 5H. pylori testing
- 6Direct antiglobulin test
- 7Testing for other autoimmune conditions
Prognosis
Good overall; children often self-resolve. Adults more likely chronic course. Fatal bleeding rare (<1%). Most maintain safe platelet counts with treatment. Quality of life considerations important. Spontaneous remission possible.
Prevention
- Avoid contact sports (if severe thrombocytopenia)
- Avoid medications that affect platelets
- Dental care to reduce bleeding risk
- Vaccinations (before splenectomy)
- Prompt treatment of infections
- Regular monitoring
Research Status
Corticosteroids first-line. IVIG for rapid response. TPO receptor agonists (eltrombopag, romiplostim) for refractory. Rituximab second-line. Splenectomy decreasing. Fostamatinib (SYK inhibitor) newer option.
Affected Countries
Sources
- https://www.hematology.org/education/patients/bleeding-disorders/immune-thrombocytopenia-itp
- https://www.mayoclinic.org/diseases-conditions/idiopathic-thrombocytopenic-purpura
- https://rarediseases.org/rare-diseases/immune-thrombocytopenic-purpura
Medical Disclaimer
This information is for educational purposes only. Always consult healthcare professionals for medical advice, diagnosis, and treatment.