DISEASE SCANNER
Global Incurable Diseases Tracker
Hemolytic Uremic Syndrome (HUS)
A serious condition affecting blood and kidneys, characterized by hemolytic anemia, thrombocytopenia, and acute kidney injury. Most commonly caused by Shiga toxin-producing E. coli (STEC) infection. Atypical HUS is complement-mediated.
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Symptoms
Treatment Options
Risk Factors
Diagnostic Methods
- 1Complete blood count
- 2Peripheral smear
- 3Bone marrow biopsy
- 4Coagulation studies
- 5Hemoglobin electrophoresis
- 6Flow cytometry
- 7Genetic testing
Prognosis
Typical HUS: excellent recovery in 85-95%. aHUS: requires eculizumab, 5-year survival 90%+. Kidney recovery variable. Recurrence risk in aHUS without prophylaxis.
Prevention
- Genetic counseling
- Nutritional adequacy
- Avoidance of triggers
- Vaccinations
- Regular monitoring
- Family screening
Research Status
Supportive care for STEC-HUS; antibiotics contraindicated. Eculizumab (complement inhibitor) for atypical HUS. Plasma exchange for severe cases. Dialysis if needed. Avoidance of STEC through food safety.
Affected Countries
Sources
- https://www.hematology.org
- https://medlineplus.gov/blooddiseases.html
- https://www.hematology.org/education/patients
- https://www.ncbi.nlm.nih.gov/books
- https://rarediseases.org/rare-diseases
Medical Disclaimer
This information is for educational purposes only. Always consult healthcare professionals for medical advice, diagnosis, and treatment.