DISEASE SCANNER
Global Incurable Diseases Tracker
Giant Cell Arteritis (Temporal Arteritis)
An inflammatory disease of blood vessels, most commonly affecting the arteries in the head, particularly the temples. Most common form of vasculitis in adults over 50. Can cause sudden blindness if untreated. Associated with polymyalgia rheumatica in 50% of cases. Affects approximately 0.5-27 per 100,000 people.
3.0M
32
Symptoms
Treatment Options
Risk Factors
Diagnostic Methods
- 1ESR (erythrocyte sedimentation rate)
- 2CRP (C-reactive protein)
- 3Temporal artery biopsy
- 4Color Doppler ultrasound
- 5MRI/MRA
- 6CT angiography
- 7Physical examination
- 8Ophthalmologic examination
Prognosis
Good with prompt treatment. Vision loss permanent if not treated urgently. Relapses occur in 50%. Treatment usually required for 1-2 years. Steroid side effects significant. Quality of life good after recovery. Life expectancy normal. Prompt recognition crucial.
Prevention
- No known prevention
- Early recognition of symptoms
- Prompt treatment prevents blindness
- Regular monitoring during treatment
- Aspirin may reduce complications
Research Status
High-dose corticosteroids immediately to prevent blindness. Tocilizumab (IL-6 inhibitor) FDA-approved. Methotrexate as steroid-sparing. Aspirin may reduce vision loss. Biopsy confirms diagnosis. Treatment typically 1-2 years. Relapses common. Urgent treatment essential.
Affected Countries
Sources
- https://www.mayoclinic.org/diseases-conditions/giant-cell-arteritis
- https://www.ncbi.nlm.nih.gov/books
- https://www.mayoclinic.org/diseases-conditions
- https://rarediseases.org/rare-diseases
Medical Disclaimer
This information is for educational purposes only. Always consult healthcare professionals for medical advice, diagnosis, and treatment.