DISEASE SCANNER
Global Incurable Diseases Tracker
Dermatomyositis
A rare inflammatory disease affecting skin and muscles, causing muscle weakness and distinctive skin rash. Belongs to a group of conditions called inflammatory myopathies. Can occur at any age but most common in adults 40-60 and children 5-15. Associated with increased cancer risk in adults.
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Symptoms
Treatment Options
Risk Factors
Diagnostic Methods
- 1Muscle enzymes (CK, aldolase)
- 2Antinuclear antibody (ANA)
- 3Myositis-specific antibodies
- 4Muscle biopsy
- 5MRI of muscles
- 6EMG (electromyography)
- 7Skin biopsy
- 8Chest CT (lung involvement)
- 9Cancer screening (adults)
Prognosis
Variable. Most respond to treatment but relapses common. Juvenile form often resolves. Adult form chronic. 20% have significant disability. Mortality increased (10-year survival 70-80%). Interstitial lung disease serious complication. Cancer surveillance essential in adults. Early treatment improves outcomes.
Prevention
- No known prevention
- Sun protection
- Early diagnosis and treatment
- Regular cancer screening (adults)
- Physical therapy to maintain function
- Avoid trigger medications
Research Status
Corticosteroids first-line treatment. Immunosuppressants (methotrexate, azathioprine). IVIG for refractory cases. Rituximab increasingly used. Sun protection essential. Physical therapy crucial. Cancer screening in adults. Topical corticosteroids for skin. Hydroxychloroquine for skin.
Affected Countries
Sources
- https://www.mayoclinic.org/diseases-conditions/dermatomyositis
- https://www.ncbi.nlm.nih.gov/books
- https://www.mayoclinic.org/diseases-conditions
- https://rarediseases.org/rare-diseases
Medical Disclaimer
This information is for educational purposes only. Always consult healthcare professionals for medical advice, diagnosis, and treatment.