DISEASE SCANNER
Global Incurable Diseases Tracker
Behçet's Disease
A rare chronic vasculitis causing recurrent mouth ulcers, genital ulcers, eye inflammation, and skin lesions. Can affect blood vessels of all sizes. Associated with HLA-B51 in some populations. Silk Road disease.
1.0M
20
Symptoms
Treatment Options
Risk Factors
Diagnostic Methods
- 1Clinical criteria
- 2Pathergy test
- 3HLA-B51 testing
- 4Eye examination
- 5Imaging (vascular, CNS)
- 6Biopsy (rarely)
Prognosis
Variable. Chronic relapsing course. Blindness possible from eye disease. Vascular and neurological complications serious. Males have worse prognosis. Lifelong management. Mortality 5-10% mainly from vascular/CNS disease.
Prevention
- No known prevention
- Early treatment
- Regular monitoring
- Avoid trauma (pathergy)
- Smoking cessation
Research Status
Colchicine first-line for mild disease. Azathioprine and cyclosporine for eye involvement. Biologics (anti-TNF, interferon-alpha) for severe disease. Apremilast (PDE4 inhibitor) for oral ulcers. Thalidomide for resistant ulcers.
Affected Countries
Sources
- https://www.mayoclinic.org/diseases-conditions/behcets-disease
- https://www.hematology.org/education/patients
- https://www.ncbi.nlm.nih.gov/books
- https://rarediseases.org/rare-diseases
Medical Disclaimer
This information is for educational purposes only. Always consult healthcare professionals for medical advice, diagnosis, and treatment.